MRKH (a.k.a. Mayer-Rokitansky-Küster-Hauser Syndrome)

So you’re a girl with MRKH (Mayer-Rokitansky-Kuster-Hauser Syndrome). It’s a hard name to write out because it is named after the four doctors who first diagnosed it (which is pretty common in the medical field.)

Girls with MRKH have two X chromosomes and no Y, so the gonads typically grow into ovaries and produce estrogen (E) and eggs.  Usually, there is enough E to help your body grow during puberty, and doctors will not give extra hormones. Since there is no womb, you won’t have a period (a.k.a. menstruate) but your hormones will probably change and your ovaries can ovulate.

In the Puberty: Outside section, check out the changes your body makes with E. Remember, your body will always have a little bit of T that comes from your adrenal glands. It may change some things, like darkening/growing of your pubic hair.

Also, in girls with MRKH, there is often a small vagina (sometimes also called a ‘dimple’), because it didn’t develop fully before birth. For more on vaginas and ways to stretch them, check out our step-to-step guide.

If you are thinking about starting dilation, talk to an experienced gynecologist to understand what is needed before you start. It’s important to involve an experienced gynecologist in this from the start. This typically means a gentle examination and working with them on a plan to go through the process of helping expand it. Everyone has different needs for their body. Talking with a doctor first is important to make sure you are doing what is right for you and your body.

For more information on MRKH, this site at About Women’s Health.Org is a great one to learn more.